This report highlights the diagnosis of an uncommon hematological condition which primarily presented to an ophthalmologist. CVT is often under diagnosed even by neurologists. It should be remembered that almost 40% of CVT patients present with signs and symptoms suggestive of isolated intracranial. A thorough diagnostic workup including magnetic resonance imaging (MRI) should be done before labeling a case as idiopathic intracranial hypertension (IIH), as the management and outcome of these two conditions vary significantly. With the increasing use of MRI in all cases suspected to be a brain syndrome, CVT has been increasing diagnosed. MRI is now the gold standard in the diagnosis of CVT as rightly done in this case.